Prague Med. Rep. 2015, 116, 181-192

Ormond’s Disease – IgG4-related Disease

Miroslav Průcha1, Ivan Kolombo2, Petr Štádler3

1Department of Clinical Biochemistry, Haematology and Immunology, Na Homolce Hospital, Prague, Czech Republic
2Department of Urology, Third Faculty of Medicine, Charles University in Prague and University Hospital Královské Vinohrady, Prague, Czech Republic
3Department of Vascular Surgery, Na Homolce Hospital, Prague, Czech Republic

Received March 9, 2015
Accepted September 15, 2015

Ormond’s disease is a relatively rare disease with unclear etiology, characterized by chronic periaortitis and retroperitoneal fibrosis. The inflammatory process affects the infrarenal part of the abdominal aorta and the iliac arteries, and the presence of infiltrates encasing the ureters and inferior vena cava. This disease is currently classed as an IgG4-related disease. In our review we analyse the clinical history, diagnostic approaches, surgical and immunosuppressive therapies.


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