Prague Med. Rep. 2020, 121, 254-261

https://doi.org/10.14712/23362936.2020.22

A Successful Treatment of Encapsulating Peritoneal Sclerosis in an Adolescent Boy on Long-term Peritoneal Dialysis: A Case Report

Zlatan Zvizdic1, Angela Summers2, Zia Moinuddin2, David Van Dellen2, Irmina Pasic-Sefic3, Faruk Skenderi4, Semir Vranic5, Titus Augustine2

1Department of Pediatric Surgery, University Clinical Center Sarajevo, Sarajevo, Bosnia and Herzegovina
2Department of Transplant and Endocrine Surgery, Manchester Royal Infirmary, Manchester University Foundation Trust; An United Kingdom National Specialized Centre for Surgery for Encapsulating Peritoneal Sclerosis, Manchester, United Kingdom
3Department of Radiology, University Clinical Center Sarajevo, Sarajevo, Bosnia and Herzegovina
4Department of Pathology, University Clinical Center Sarajevo, Sarajevo, Bosnia and Herzegovina
5College of Medicine, QU Health, Qatar University, Qatar

Received April 10, 2020
Accepted November 2, 2020

Encapsulating peritoneal sclerosis (EPS) is a rare life-threatening complication associated with peritoneal dialysis (PD). EPS is characterized by progressive fibrosis and sclerosis of the peritoneum, with the formation of a membrane and tethering of loops of the small intestine resulting in intestinal obstruction. It is very rare in children. We present a case of a 16-year-old adolescent boy who developed EPS seven years after being placed on continuous ambulatory peritoneal dialysis (CAPD) complicated by several episodes of bacterial peritonitis. The diagnosis was based on clinical, radiological, intraoperative and histopathological findings. The patient was successfully treated with surgical enterolysis. During a 7-year follow-up, there have been no further episodes of small bowel obstruction documented. He still continues to be on regular hemodialysis and is awaiting a deceased donor kidney transplant. EPS is a long-term complication of peritoneal dialysis and is typically seen in adults. Rare cases may be seen in the pediatric population and require an appropriate surgical approach that is effective and lifesaving for these patients.

References

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