Prague Med. Rep. 2025, 126, 238-242
Freeman-Sheldon Syndrome: A Rare Case Report with Dental Perspective
, Nikil Kumar Jain2, Sudhir Ramesh Maheshkar2
1Department of Oral Medicine and Radiology, Shree Bankey Bihari Dental College and Research Center, Ghaziabad, India
2Department of Oral and Maxillofacial Surgery, Awadh Dental College and Hospital, Jamshedpur, India
Received December 12, 2024
Accepted November 21, 2025
Freeman-Sheldon syndrome is a rare form of multiple congenital contracture syndromes (arthrogryposes) and is the most severe form of distal arthrogryposis. The main skeletal malformations include camptodactyly with ulnar deviation and talipes equinovarus while facial characteristics include deep-sunken eyes with hypertelorism, increased philtrum length, small nose and nostrils, and a small mouth. Here we report a rare case of Freeman-Sheldon syndrome (FSS) in an 8-years-old patient giving emphasis on the dental management of FSS.
Keywords
Freeman-Sheldon syndrome, Distal arthrogryposis, Skeletal malformations, Oro facial features, Dental management.
References
Copyright
This is an open-access article distributed under the terms of the Creative Commons Attribution License.
