Prague Med. Rep. 2024, 125, 69-78
Gorlin-Goltz Syndrome – A Rare Case Entity in Young Child
Gorlin-Goltz syndrome (GGS) is an infrequent multisystemic disease with an autosomal dominant trait, which depicted presence of numerous basal cell carcinoma in conjunction with multiorgan abnormalities. This syndrome may be diagnosed early by a dentist by routine radiographic exams in the first decade of life, since the keratocystic odontogenic tumour are usually one of the first manifestations of the syndrome. This article includes a case report of the GGS with regard to its history, incidence, etiology, features, investigations, diagnostic criteria, keratocystic odontogenic tumour and treatment modalities.
Keywords
Nevoid basal cell carcinoma, Odontogenic keratocyst, Carnoy’s solution, “En-bloc” resection, Marsupialization, Bifid rib.
References
Copyright
This is an open-access article distributed under the terms of the Creative Commons Attribution License.
