Prague Med. Rep. 2024, 125, 69-78

Gorlin-Goltz Syndrome – A Rare Case Entity in Young Child

Shovita Mondal1, Nikil Kumar Jain1, Abhishek Dutta1, Nishant1, Abhijit Dutta2, Moushumi Shil1, Suman Sen3

1Department of Oral and Maxillofacial Surgery, Awadh Dental College, Jamshedpur, Jharkhand, India
2Department of Oral and Maxillofacial Pathology and Microbiology, Awadh Dental College, Jamshedpur, Jharkhand, India
3Department of Oral Medicine and Radiology, Haldia Institute of Dental Science and Research, Haldia, West Bengal, India

Received August 14, 2023
Accepted January 30, 2024

Gorlin-Goltz syndrome (GGS) is an infrequent multisystemic disease with an autosomal dominant trait, which depicted presence of numerous basal cell carcinoma in conjunction with multiorgan abnormalities. This syndrome may be diagnosed early by a dentist by routine radiographic exams in the first decade of life, since the keratocystic odontogenic tumour are usually one of the first manifestations of the syndrome. This article includes a case report of the GGS with regard to its history, incidence, etiology, features, investigations, diagnostic criteria, keratocystic odontogenic tumour and treatment modalities.


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