Prague Med. Rep. 2024, 125, 130-137

https://doi.org/10.14712/23362936.2024.11

A Severe and Fatal Type A Aortic Dissection in an Adult with a Repaired Tetralogy of Fallot

Manuela Montatore1, Federica Masino1, Vincenzo Signorile2, Marina Balbino1, Ruggiero Tupputi3, Giuseppe Guglielmi1,3,4

1Department of Clinical and Experimental Medicine, Foggia University School of Medicine, Foggia, Italy
2Cardiology Unit, Anthea Hospital, Bari, Italy
3Radiology Unit, “Dimiccoli” Hospital, Barletta, Italy
4Radiology Unit, “IRCCS Casa Sollievo della Sofferenza” Hospital, San Giovanni Rotondo, Italy

Received January 30, 2024
Accepted May 7, 2024

We report a case of a 44-year-old woman surgically treated for tetralogy of Fallot who experienced an acute and extensive Stanford A type aortic dissection despite the meticulous follow-up. While aortic dilatation is prevalent in individuals with repaired tetralogy of Fallot, aortic dissection represents a rare consequence, that when it appears, is progressive and usually detected during the check-up visits. In the case reported, the dissection was unexpected and severe, and the patient’s clinical state worsened suddenly, leading to death after a few days. Constant awareness for aortic aneurysms is essential in the Fallot tetralogy population, nevertheless, several causes may contribute to the acute worsening of the clinical condition until the patient’s death.

References

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